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Vasculitis

The new look of classification criteria for systemic vasculitis

Nature Reviews Rheumatology volume 19, pages 198–199 (2023)Cite this article

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An ambitious project to update the classification of vasculitis syndromes has culminated in the development of new classification criteria for anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitis, Takayasu arteritis and giant cell arteritis. Endorsed by the ACR and EULAR, the new criteria reflect progress in the understanding and assessment of these conditions.

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Fig. 1: Timeline of the nomenclature and classification criteria of systemic vasculitis.

References

  1. Watts, R. A. Evolving concepts in classification of systemic vasculitis: where are we and what is the way forward? Int. J. Rheum. Dis. 22 (Suppl. 1), 21–27 (2019).

    Article  PubMed  Google Scholar 

  2. Grayson, P. C. et al. 2022 American College of Rheumatology/European Alliance of Associations for Rheumatology classification criteria for eosinophilic granulomatosis with polyangiitis. Ann. Rheum. Dis. 81, 309–314 (2022).

    Article  PubMed  Google Scholar 

  3. Robson, J. C. et al. 2022 American College of Rheumatology/European Alliance of Associations for Rheumatology classification criteria for granulomatosis with polyangiitis. Ann. Rheum. Dis. 81, 315–320 (2022).

    Article  PubMed  Google Scholar 

  4. Suppiah, R. et al. 2022 American College of Rheumatology/European Alliance of Associations for Rheumatology classification criteria for microscopic polyangiitis. Arthritis Rheumatol. 74, 400–406 (2022).

    Article  CAS  PubMed  Google Scholar 

  5. Ponte, C. et al. 2022 American College of Rheumatology/EULAR classification criteria for giant cell arteritis. Arthritis Rheumatol. 74, 1881–1889 (2022).

    Article  CAS  PubMed  Google Scholar 

  6. Grayson, P. C. et al. 2022 American College of Rheumatology/EULAR classification criteria for Takayasu arteritis. Ann. Rheum. Dis. 81, 1654–1660 (2022).

    Article  PubMed  Google Scholar 

  7. Wallace, Z. S. et al. The 2019 American College of Rheumatology/European League Against Rheumatism classification criteria for IgG4-related disease. Arthritis Rheumatol. 72, 7–19 (2020).

    Article  PubMed  Google Scholar 

  8. Mahr, A., Specks, U. & Jayne, D. Subclassifying ANCA-associated vasculitis: a unifying view of disease spectrum. Rheumatology (Oxford) 58, 1707–1709 (2019).

    Article  PubMed  Google Scholar 

  9. Koster, M. J., Matteson, E. L. & Warrington, K. J. Large-vessel giant cell arteritis: diagnosis, monitoring and management. Rheumatology (Oxford) 57 (Suppl. 2), ii32–ii42 (2018).

    Article  CAS  PubMed  Google Scholar 

  10. Beck, D. B. et al. Somatic mutations in UBA1 and severe adult-onset autoinflammatory disease. N. Engl. J. Med. 383, 2628–2638 (2020).

    Article  CAS  PubMed  PubMed Central  Google Scholar 

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Authors and Affiliations

  1. Department of Experimental and Clinical Medicine, University of Firenze, Firenze, Italy

    Giacomo Emmi

  2. Centre for Inflammatory Diseases, Monash University Department of Medicine, Monash Medical Centre, Clayton, Australia

    Giacomo Emmi

  3. Nephrology and Dialysis Unit, Azienda Ospedaliera Universitaria Meyer IRCCS, Firenze, Italy

    Augusto Vaglio

  4. Department of Biomedical, Experimental and Clinical Sciences “Mario Serio”, University of Firenze, Firenze, Italy

    Augusto Vaglio

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  1. Giacomo Emmi
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  2. Augusto Vaglio
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Correspondence to Augusto Vaglio.

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Emmi, G., Vaglio, A. The new look of classification criteria for systemic vasculitis. Nat Rev Rheumatol 19, 198–199 (2023). https://doi.org/10.1038/s41584-023-00933-5

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